Moyamoya syndrome in a child with HbEβ-thalassemia

Akmal Zahra 1, Hanan Al-Abboh 1, Yousif Habeeb 2, Adekunle Adekile 1 3

Affiliations

08 March 2022

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doi: 10.1002/ccr3.5536

Abstract

Moyamoya is a progressive cerebrovascular disease associated with stenosis or occlusion of the arteries of the Circle of Willis. It is uncommon in thalassemia. We present a 9-year-old girl with HbEβ-thalassemia who presented with headache, vomiting, and episodes of transient hemiparesis with complete occlusion internal carotid arteries.

Keywords: Moyamoya; cerebral infarcts; seizures; thalassemia.

Conflict of interest statement

The authors have no conflict of interest to declare.

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