Moyamoya syndrome in a child with HbEβ-thalassemia

Akmal Zahra 1, Hanan Al-Abboh 1, Yousif Habeeb 2, Adekunle Adekile 1 3

Affiliations

08 March 2022

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doi: 10.1002/ccr3.5536

Abstract

Moyamoya is a progressive cerebrovascular disease associated with stenosis or occlusion of the arteries of the Circle of Willis. It is uncommon in thalassemia. We present a 9-year-old girl with HbEβ-thalassemia who presented with headache, vomiting, and episodes of transient hemiparesis with complete occlusion internal carotid arteries.

Keywords: Moyamoya; cerebral infarcts; seizures; thalassemia.

Figures

FIGURE 1 Magnetic resonance angiography showing occlusion of both internal carotid arteries (arrow) at the cavernous segment

FIGURE 1 Magnetic resonance angiography showing occlusion of both internal carotid arteries (arrow) at the cavernous segment

FIGURE 2 Magnetic resonance angiography showing occlusion (open arrow heads) of both internal carotid arteries. The internal carotid (round arrow heads) caliber is reduced, whereas that of the vertebral arteries (double headed arrow) and basilar arteries (arrow head) are increased

FIGURE 2 Magnetic resonance angiography showing occlusion (open arrow heads) of both internal carotid arteries. The internal carotid (round arrow heads) caliber is reduced, whereas that of the vertebral arteries (double headed arrow) and basilar arteries (arrow head) are increased

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